Department of Maxillofacial Surgery, University of Zagreb School of Medicine and School of Dental Medicine, University Hospital Dubrava, Zagreb, Croatia.
J Craniomaxillofac Surg. 2011 Sep;39(6):445-8. doi: 10.1016/j.jcms.2010.10.010. Epub 2010 Nov 11.
Synovial sarcoma (SS) is a malignant mesenchymal tumour, predominantly found in the deep soft tissues of lower extremities, whereas only 3% occur in the head and neck region. Primary synovial sarcoma of the parotid gland is exceptionally uncommon. This is a report of a 15-year-old boy with a synovial sarcoma arising in the parotid gland, and, to the best of our knowledge, this is the youngest patient on record. The patient was treated primarily surgically, followed by chemotherapy and radiotherapy. Two years after this multimodal therapy, the patient is without signs of loco-regional recurrence or distant metastases. This paper highlights the importance of a multidisciplinary approach in the diagnosis and treatment of this very rare entity.
滑膜肉瘤(SS)是一种恶性间叶组织肿瘤,主要发生于下肢深部软组织,而仅有 3%发生于头颈部。原发于腮腺的滑膜肉瘤极其罕见。本文报道了一例 15 岁男性患者,其腮腺发生滑膜肉瘤,据我们所知,这是有记录以来最年轻的患者。该患者主要接受了手术治疗,随后进行了化疗和放疗。经过这种多模式治疗两年后,患者无局部区域复发或远处转移的迹象。本文强调了多学科方法在诊断和治疗这种非常罕见实体瘤中的重要性。