Milone Luca, Okhunov Zhamshid, Gumbs Andrew A
Department of Surgical Oncology, Fox Chase Cancer Center, Philadelphia, PA, USA.
J Gastrointest Cancer. 2012 Jun;43(2):367-9. doi: 10.1007/s12029-010-9232-2.
Annular pancreas (AP) is a rare anomaly due to malrotation of the pancreatic ventral bud during embryologic development. AP has been extensively described in the pediatric population; however, in adults, the incidence has been reported to be only 1 in 22,000 patients with only a few cases presenting with simultaneous mucinous cystadenoma described in the recent literature.
We report the case of a 72-year-old female patient with a mucinous cystadenoma, who was found to have a concomitant AP during laparoscopic distal pancreatectomy.
The dual presentation of annual pancreas and mucinous cystoadenoma is an infrequent condition and can be managed with minimally invasive techniques; bypass in adults should only be performed in patients with symptomatic duodenal compression or recurrent bouts of pancreatitis.
环状胰腺(AP)是一种由于胚胎发育过程中胰腹侧芽旋转异常导致的罕见畸形。AP在儿科人群中已有广泛描述;然而,在成人中,据报道发病率仅为22000分之一,近期文献中仅描述了少数同时伴有黏液性囊腺瘤的病例。
我们报告一例72岁女性患者,患有黏液性囊腺瘤,在腹腔镜远端胰腺切除术中发现同时伴有AP。
环状胰腺和黏液性囊腺瘤的双重表现并不常见,可采用微创技术进行处理;成人中仅在有症状性十二指肠压迫或复发性胰腺炎发作的患者中进行旁路手术。