Pontes Hélder Antônio Rebelo, Pontes Flávia Sirotheau Corrêa, Cruz e Silva Bruno Thiago, Fonseca Felipe Paiva, Carneiro José Thiers, Paiva Helena Borges, Pinto Décio dos Santos
João de Barros Barreto University Hospital, Federal University of Pará, Pará, Brazil.
J Craniofac Surg. 2010 Nov;21(6):1984-7. doi: 10.1097/SCS.0b013e3181f503be.
Neurofibroma is a benign peripheral nerve sheath tumor that can be occasionally found in the head and neck region as multiple lesions associated with neurofibromatosis type 1 (NF-1) or as a solitary tumor. The real frequency of isolated neurofibromas not associated with NF is uncertain, and lesions in the temporal region are extremely rare. The aim of the current article was to report an unusual case of solitary neurofibroma localized in the temporal and infratemporal regions with 10 years of evolution in a female patient without any other manifestation or familiar history of NF-1. The patient underwent surgical treatment for complete excision of the lesion, and the 2-year follow-up revealed no signs of recurrence.
神经纤维瘤是一种良性周围神经鞘瘤,偶尔可在头颈部发现,表现为与1型神经纤维瘤病(NF-1)相关的多发病变或孤立性肿瘤。与NF无关的孤立性神经纤维瘤的实际发生率尚不确定,颞区的病变极为罕见。本文旨在报告一例罕见的孤立性神经纤维瘤病例,该肿瘤位于颞区和颞下区,在一名无任何其他NF-1表现或家族史的女性患者中已发展了10年。患者接受了手术治疗以完全切除病变,2年的随访显示无复发迹象。