Department of Pathology at Fletcher Allen Health Care, University of Vermont, College of Medicine, Burlington, VT 05401, USA.
Int J Gynecol Pathol. 2011 Jan;30(1):71-5. doi: 10.1097/PGP.0b013e3181efe08d.
Lymphangioleiomyomatosis (LAM) is part of a family of lesions collectively known as perivascular epithelioid cell neoplasms (PEComas). Though these lesions are comprised of histologically and immunohistochemically distinctive perivascular epithelioid cells, their diagnosis is controversial and some investigators question their existence entirely. We present a unique case of perhaps the earliest microscopic example of a LAM PEComa in the uterine myometrium, and contrast its features to that of intravascular adenomyosis, intravascular endometrial stromal sarcoma, and intravascular leiomyoma.
淋巴管平滑肌瘤病（LAM）是一组被称为血管周围上皮样细胞肿瘤（PEComas）的病变的一部分。尽管这些病变由组织学和免疫组织化学上独特的血管周围上皮样细胞组成，但它们的诊断存在争议，一些研究人员完全质疑它们的存在。我们提出了一个独特的病例，可能是子宫子宫肌层中最早的 LAM PEComa 的微观范例，并将其特征与血管内腺肌病、血管内子宫内膜间质肉瘤和血管内平滑肌瘤进行对比。
