Polat Muhterem, Polat Fazli, Oztaş Pinar, Kaya Canan, Alli Nuran
First Dermatology Department, Ankara Numune Education and Research Hospital, Ankara, Turkey.
Skinmed. 2010 May-Jun;8(3):181-3.
A 10-year-old girl who was admitted to the urology department with complaints of urinary incontinence was referred to our dermatology outpatient clinic because of a congenital, circumscribed, hypertrichotic area on the lumbosacral region. Cutaneous examination revealed a circumscribed area of coarse, dark terminal hair measuring 25 x 15 cm overlying the lumbosacral area with normal underlying skin (Figure 1). There were erythematous macular lesions on the superior of the hairy area. The lesion had been present since birth, and no other family member had similar lesions. Her history revealed back pain and a long history of urinary incontinence. On neurologic examination, no motor weakness or sensory changes were observed. Babinski reflex was positive on the left. Magnetic resonance imaging (MRI) findings included diastematomyelia between T12 and L1 levels and slight flattening of lumbar lordosis (Figure 2). A diagnosis of faun tail with underlying spinal dysraphism was made. There was also urinary incontinence as late sequelae of spinal dysraphism.
一名因尿失禁主诉入住泌尿外科的10岁女孩，因腰骶部先天性、局限性多毛区域被转诊至我们皮肤科门诊。皮肤检查发现，腰骶部有一个边界清楚的粗糙、深色终毛区域，大小为25×15厘米，其下方皮肤正常（图1）。多毛区域上方有红斑性斑疹病变。该病变自出生就存在，且没有其他家庭成员有类似病变。她的病史显示有背痛和长期尿失禁史。神经系统检查未发现运动无力或感觉改变。左侧巴宾斯基征阳性。磁共振成像（MRI）结果包括胸12至腰1水平的脊髓纵裂和腰椎前凸轻度变平（图2）。诊断为伴有潜在脊柱发育异常的藏毛窦。还存在作为脊柱发育异常晚期后遗症的尿失禁。
