一名男孩出现会阴瘘，诊断为Y型重复尿道。
Y-type urethral duplication presented with perineal fistula in a boy.
作者信息
Dayanc Murat, Irkilata Hasan Cem, Kibar Yusuf, Bozkurt Yasar, Basal Seref, Xhafa Ajet
机构信息
Gulhane Military Medical Academy, Department of Urology, Ankara, Turkey.
出版信息
Ger Med Sci. 2010 Nov 29;8:Doc33. doi: 10.3205/000122.
Abstract
Urethral duplication is a rare congenital anomaly of the lower urinary system and has varied presentation. According to the Effmann classification, type IIA2-Y urethral duplication is characterized by the duplicated urethra originating from the bladder neck and opening into either the rectum or the perineum. The accessory urethra is normal and functional and the normally positioned dorsal urethra is hypoplastic and stenotic in unusual form of Y-type duplication. We present a new case with unusual form of Y-type duplication and discuss its treatment.
摘要
尿道重复是下泌尿系统一种罕见的先天性异常，表现多样。根据埃夫曼分类法，IIA2 - Y型尿道重复的特征是重复尿道起源于膀胱颈，开口于直肠或会阴。副尿道正常且有功能，而正常位置的背侧尿道发育不全且狭窄，呈不寻常的Y型重复形式。我们报告一例不寻常形式的Y型重复病例并讨论其治疗方法。
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