Viart P, Deuvaert F, Gallez A, Primo G, Dramaix M
Unité médico-chirurgicale de cardiologie, hôpital universitaire des Enfants Reine Fabiola, Bruxelles, Belgique.
Arch Mal Coeur Vaiss. 1990 May;83(5):653-7.
The late results of 115 children with tetralogy of Fallot born and corrected between 1969 and 1988 are analyzed; the patients were distributed into 3 anatomical groups: normal pulmonary annulus (group A, 49 patients) annular stenosis (group B, 56 patients) and pulmonary atresia (group C, 10 patients). The probability of survival 15 years after correction is 97 p. 100 in cumulated groups A and B and 72 p. 100 in group C (p = 0.005). The probability of reoperation ten years after correction is 4 p. 100 in cumulated groups A and B without a previous shunt, 20 p. 100 in A and B with a previous shunt (p less than 0.05) and 55 p. 100 in group C (p = 0.0004). The proportion of serious cardiac sequellae amounts to 17 p. 100 in group A, 55 p. 100 in group B and 100 p. 100 in group C (p = 0.0005). As a whole, 55 p. 100 of the adolescents operated on for tetralogy of Fallot during infancy present a residual problem of some severity.
分析了1969年至1988年间出生并接受矫正手术的115例法洛四联症患儿的远期结果；这些患者被分为3个解剖学组：正常肺动脉瓣环（A组，49例患者）、瓣环狭窄（B组，56例患者）和肺动脉闭锁（C组，10例患者）。矫正术后15年的累积生存率在A组和B组为97%，在C组为72%（p = 0.005）。矫正术后10年再次手术的概率，在A组和B组累积且未行分流术的患者中为4%，在A组和B组曾行分流术的患者中为20%（p < 0.05），在C组中为55%（p = 0.0004）。严重心脏后遗症的比例在A组为17%，在B组为55%，在C组为100%（p = 0.0005）。总体而言，婴儿期接受法洛四联症手术的青少年中有55%存在某种程度的残留问题。
