Tabuchi H, Kawai N, Nagasaka Y
Department of Internal Medicine, Shinkawabata Hospital.
Kokyu To Junkan. 1990 May;38(5):493-6.
A 56-year-old male with moderate pulmonary hypertension associated with liver cirrhosis was treated successfully by long term oxygen and vasodilator therapy. Improvement of pulmonary hypertension and clinical symptoms were proved by chest X-ray, ECG, echocardiography and right heart catheterization. Hegglin's phenomenon confirmed by phono- and mechanocardiography may suggest a hyperkinetic state as well as the so-called "energischemetabolische Herzinsufficienz" related to liver cirrhosis. The patient was treated for 18 months. After 2 months of therapy the patient became asymptomatic during modest daily activity, and apparent improvements of hemodynamic parameters were observed thereafter. Long term oxygen and vasodilator therapy in this patient with pulmonary hypertension associated with liver cirrhosis proved as effective as it has been in patients with primary pulmonary hypertension.
一名56岁男性，患有与肝硬化相关的中度肺动脉高压，通过长期吸氧和血管扩张剂治疗获得成功。胸部X光、心电图、超声心动图和右心导管检查证实肺动脉高压和临床症状有所改善。心音图和机械心动图证实的赫格利现象可能提示高动力状态以及与肝硬化相关的所谓“能量代谢性心力衰竭”。该患者接受了18个月的治疗。治疗2个月后，患者在适度日常活动时无症状，此后观察到血流动力学参数有明显改善。对这名患有与肝硬化相关的肺动脉高压的患者进行长期吸氧和血管扩张剂治疗，证明与原发性肺动脉高压患者的治疗效果一样有效。
