Department of Dental Anesthesiology, Tokyo Dental College, 1-2-2 Masago, Mihama-ku, Chiba 261-8502, Japan.
J Anesth. 2011 Feb;25(1):123-6. doi: 10.1007/s00540-010-1059-2. Epub 2010 Dec 9.
Aicardi syndrome (AS) is a rare congenital syndrome and is characterized by the triad of infantile spasm, agenesis of the corpus callosum, and anomaly of chorioretinal lacunae. We here report a case of a patient with AS under general anesthesia. Although there is no report in which muscle relaxants were used in AS patients, vecuronium bromide was used for artificial pneumoperitoneum in this case. Careful management is important for AS patients during an operation that significantly affects respiratory function. In addition, it is possible that muscle relaxants be administered safely in AS patients. Careful monitoring such as epileptiform electroencephalogram and bispectral index monitors may be needed for the early detection of epileptic activities.
Aicardi 综合征(AS)是一种罕见的先天性综合征,其特征为婴儿痉挛、胼胝体发育不全和脉络膜视网膜裂孔畸形三联征。我们在此报告一例全身麻醉下的 AS 患者病例。虽然没有 AS 患者使用肌松剂的报道,但本病例在人工气腹时使用了维库溴铵。对于明显影响呼吸功能的手术,对 AS 患者进行仔细的管理非常重要。此外,肌松剂在 AS 患者中可能安全使用。可能需要使用癫痫样脑电图和双频谱指数监测器等进行仔细监测,以早期发现癫痫活动。