Division of Hematology and Oncology, University of Pennsylvania, Philadelphia, Pennsylvania, USA.
J Clin Invest. 2011 Jan;121(1):22-5. doi: 10.1172/JCI43605. Epub 2010 Dec 13.
Chronic myeloid leukemia (CML) is a hematopoietic disease characterized by expansion of myeloid blood cells. It is caused by the t(9;22) chromosomal translocation that results in the expression of the fusion tyrosine kinase BCR-ABL. Tyrosine kinase inhibitor (TKI) therapy has led to long-term remissions, but patients remain BCR-ABL+. There is agreement that TKIs do not kill CML stem cells; however, it is controversial whether this is because of a lack of BCR-ABL kinase inhibition in CML stem cells or because CML stem cells do not require BCR-ABL for survival. In this issue of the JCI, Corbin and colleagues provide definitive evidence that BCR-ABL is kinase active in CML stem cells and that TKIs inhibit this kinase activity without affecting CML stem cell survival. Rather, CML stem cells revert to a normal dependence on cytokines for survival and proliferation. These results demonstrate that the CML stem cell is not BCR-ABL addicted and have important implications for developing curative therapeutic approaches to CML.
慢性髓性白血病(CML)是一种造血系统疾病,其特征是髓系血细胞的扩增。它是由 t(9;22)染色体易位引起的,导致融合酪氨酸激酶 BCR-ABL 的表达。酪氨酸激酶抑制剂(TKI)治疗导致了长期缓解,但患者仍然存在 BCR-ABL+。人们一致认为 TKI 不会杀死 CML 干细胞;然而,这是因为 CML 干细胞中缺乏 BCR-ABL 激酶抑制,还是因为 CML 干细胞的生存不需要 BCR-ABL,这是有争议的。在本期 JCI 中,Corbin 及其同事提供了明确的证据,证明 BCR-ABL 在 CML 干细胞中具有激酶活性,TKI 抑制这种激酶活性而不影响 CML 干细胞的存活。相反,CML 干细胞恢复到对细胞因子的正常依赖以维持生存和增殖。这些结果表明,CML 干细胞不是 BCR-ABL 成瘾的,这对开发治疗 CML 的治愈性治疗方法具有重要意义。