Ozgur Senem, Senocak Filiz, Orun Utku Arman, Ocal Burhan, Karademir Selmin, Dogan Vehbi, Yilmaz Osman
Dr. Sami Ulus Children Hospital, Babur Street No: 44, Altindag, Ankara, Turkey.
Interact Cardiovasc Thorac Surg. 2011 Mar;12(3):370-3. doi: 10.1510/icvts.2010.246694. Epub 2010 Dec 20.
Isolated left ventricular non-compaction (LVNC) is a rare cardiomyopathy characterized by prominent trabeculations and deep intratrabecular recesses. In this study, we aimed to identify the clinical characteristics of children with ventricular non-compaction and determine the factors affecting prognosis. We retrospectively evaluated 29 children with LVNC followed at Dr. Sami Ulus Children Hospital Pediatric Cardiology Department from December 2004 to November 2009. There were 13 females (45%) and 16 males (55%) and the mean age at presentation was 4.8±4.6 years (one month-15 years). Although there was no statistical significance; early presentation age and high left ventricular end-diastolic diameter at the diagnosis were associated with poorer prognosis.
孤立性左心室心肌致密化不全（LVNC）是一种罕见的心肌病，其特征为显著的肌小梁和深陷的小梁内隐窝。在本研究中，我们旨在确定心室心肌致密化不全患儿的临床特征，并确定影响预后的因素。我们回顾性评估了2004年12月至2009年11月在萨米·乌卢斯博士儿童医院儿科心脏病科随访的29例LVNC患儿。其中女性13例（45%），男性16例（55%），就诊时的平均年龄为4.8±4.6岁（1个月至15岁）。虽然无统计学意义，但发病年龄早和诊断时左心室舒张末期内径大与预后较差相关。
