Bukkems S F, Stoot J H, Driessen A, Beets-Tan R G, van Nieuwenhoven M A, Masclee A M
Department of Surgery, Maastricht University Medical Centre, Maastricht, the Netherlands.
Neth J Med. 2010 Dec;68(12):414-7.
We present the case of a patient with the rare triad of Von Recklinghausen's disease associated with a somatostatinoma and a gastrointestinal stromal tumour (GIST). The patient had recurrent jaundice, the typical somatostatinoma syndrome, positive MR imaging but negative ⁶⁸Ga-DOTATOC PET scanning in a histopathology-proven somatostatinoma tumour.
我们报告了一例患有冯·雷克林豪森病罕见三联征的患者，该三联征与生长抑素瘤和胃肠道间质瘤（GIST）相关。患者有复发性黄疸，典型的生长抑素瘤综合征，磁共振成像（MR）呈阳性，但在经组织病理学证实的生长抑素瘤肿瘤中，⁶⁸Ga-DOTATOC正电子发射断层扫描（PET）呈阴性。
