Takeshita Kyosuke, Inden Yasuya, Murohara Toyoaki
Department of Cardiology, Nagoya University Graduate School of Medicine, Aichi 466-8550, Nagoya, Japan.
Eur J Echocardiogr. 2011 Mar;12(3):E26. doi: 10.1093/ejechocard/jeq188. Epub 2011 Jan 6.
Double-orifice mitral valve (DOMV) is an uncommon congenital malformation characterized by two valve orifices with two separate subvalvular structures. Double-orifice mitral valve is usually associated with various other congenital malformations and isolated DOMV is rare. We describe here two adult cases of DOMV without any other malformations, examined by two- and three-dimensional echocardiography for detailed evaluation of the mitral valve and subvalvular structures. We stress the need for careful imaging of the mitral valve by three-dimensional echocardiography even in patients free of other congenital heart anomalies.
双孔二尖瓣（DOMV）是一种罕见的先天性畸形，其特征为有两个瓣口及两个独立的瓣下结构。双孔二尖瓣通常与各种其他先天性畸形相关，孤立性双孔二尖瓣很少见。我们在此描述两例无任何其他畸形的成年双孔二尖瓣病例，通过二维和三维超声心动图对二尖瓣及瓣下结构进行详细评估。我们强调，即使对于无其他先天性心脏异常的患者，也需要通过三维超声心动图对二尖瓣进行仔细成像。
