Huang Chuang-Chi, Ma Cheng-Jen, Huang Wan-Ting, Chan Te-Fu, Wang Jaw-Yuan
Department of Surgery, Kaohsiung Medical University Hospital, Kaohsiung Medical University, Kaohsiung, Taiwan.
J Med Case Rep. 2011 Jan 18;5:15. doi: 10.1186/1752-1947-5-15.
Extragenital malignant mixed Müllerian tumor is an extremely rare presentation of malignant mixed Müllerian tumor, especially when combined with a synchronous ovarian cancer.
We report the clinical course and pathologic findings of a case of mesorectal malignant mixed Müllerian tumor with synchronous ovarian cancer, in a 50-year-old, gravida 0, para 0, Han Chinese woman with regular menstruation. This is the sixteenth case in the English literature of extragenital malignant mixed Müllerian tumor combined with synchronous or metachronous malignancy reported.
Although extragenital malignant mixed Müllerian tumor is very rare and has a poor prognososis, a longer survival time might be achieved with treatment by cytoreductive surgery, radiotherapy and chemotherapy.
生殖器外恶性混合性苗勒管肿瘤是恶性混合性苗勒管肿瘤的一种极其罕见的表现形式,尤其是当它与同步发生的卵巢癌合并时。
我们报告了一例50岁、孕0产0、月经规律的汉族女性直肠系膜恶性混合性苗勒管肿瘤合并同步卵巢癌的临床病程及病理结果。这是英文文献中报道的第16例生殖器外恶性混合性苗勒管肿瘤合并同步或异时性恶性肿瘤的病例。
尽管生殖器外恶性混合性苗勒管肿瘤非常罕见且预后较差,但通过减瘤手术、放疗和化疗等治疗手段可能会获得更长的生存时间。