Jamjoom Z A, Malabarey T, Kolawole T M, Araby K
Division of Neurosurgery, College of Medicine, King Saud University, Riyadh, Saudi Arabia.
Acta Neurochir (Wien). 1990;105(3-4):140-6. doi: 10.1007/BF01669998.
The lumbosacral dural abnormalities in two patients with von Recklinghausen neurofibromatosis (vRNF) are described. Analysis of 18 previously reported cases revealed considerable morphological variations of the lumbosacral dural lesions associated with vRNF, but three basic forms may be distinguished. The pathogenesis of these lesions is still controversial. The contrast studies in our patients, especially the computed tomographic myelography (CTM), suggest that the meningocoeles in vRNF are, in fact, abnormally dilated and elongated nerve root sleeves and should, therefore, be distinguished from other types of meningeal cysts occurring in the lumbosacral region. The clinical significance of these dural anomalies are discussed.
本文描述了两名患有冯雷克林霍增氏神经纤维瘤病（vRNF）患者的腰骶部硬脊膜异常情况。对18例既往报道病例的分析显示，与vRNF相关的腰骶部硬脊膜病变在形态上有相当大的差异，但可区分出三种基本形式。这些病变的发病机制仍存在争议。我们患者的对比研究，尤其是计算机断层脊髓造影（CTM）表明，vRNF中的脊膜膨出实际上是异常扩张和延长的神经根袖套，因此，应与腰骶部出现的其他类型的脑膜囊肿相区分。本文讨论了这些硬脊膜异常的临床意义。
