Stefanidis Konstantinos, Benakis Stelios, Tsatalou Emmanouela, Ouranos Vasilios, Chondros Dimitrios
CT and MRI department, Evangelismos Hospital, Ipsilantou 45-47, 10676, Athens, Greece.
J Med Case Rep. 2011 Jan 24;5:28. doi: 10.1186/1752-1947-5-28.
Desmoplastic fibroma is an extremely rare primary benign bone tumor. It occurs most often in the mandible, followed by the femur and pelvis. To the best of our knowledge, fewer than 200 cases have been described in the published literature. Furthermore, this case is the first report of desmoplastic fibroma with simultaneous presentation in two different locations.
We present an unusual case of desmoplastic fibroma in a 56-year-old Caucasian man, who presented to our hospital with lumbar pain. Computed tomography and magnetic resonance imaging were performed, demonstrating two lytic expansile lesions affecting both his left iliac bone and his left sacral wing. Curettage and cortical-cancellous grafting was performed, followed by postoperative computed tomography and magnetic resonance imaging.
Desmoplastic fibroma with unusual and simultaneous manifestations in two different locations has never been reported previously to the best of our knowledge. The purpose of this case report is to present the computed tomography and magnetic resonance imaging features of this rare tumor before and after the surgical treatment. Furthermore, the radiological findings with the description of the characteristics and the clinical presentation of this rare tumor, contribute to the wide spectrum of manifestations of this tumor, in order to recognize it and to have the appropriate management.
促结缔组织增生性纤维瘤是一种极其罕见的原发性良性骨肿瘤。它最常发生于下颌骨,其次是股骨和骨盆。据我们所知,已发表的文献中描述的病例少于200例。此外,该病例是促结缔组织增生性纤维瘤同时出现在两个不同部位的首例报告。
我们报告一例56岁白种男性的促结缔组织增生性纤维瘤罕见病例,该患者因腰痛前来我院就诊。进行了计算机断层扫描和磁共振成像检查,显示两个溶骨性膨胀性病变,累及左侧髂骨和左侧骶骨翼。进行了刮除术和皮质-松质骨移植,术后进行了计算机断层扫描和磁共振成像检查。
据我们所知,促结缔组织增生性纤维瘤在两个不同部位出现异常且同时出现的表现此前从未有过报道。本病例报告的目的是展示这种罕见肿瘤在手术治疗前后的计算机断层扫描和磁共振成像特征。此外,该罕见肿瘤的影像学表现以及特征和临床表现的描述,有助于了解该肿瘤广泛的表现形式,以便识别并进行适当的处理。