Ishii Yoichiro, Miyamoto Takashi, Kobayashi Tohru, Kobayashi Tomio
Department of Cardiology, Gunma Children's Medical Center, 779 Shimohakoda, Hokkitsu-machi, Shibukawa, Gunma, 377-8577, Japan.
Pediatr Cardiol. 2011 Apr;32(4):509-11. doi: 10.1007/s00246-011-9887-x. Epub 2011 Jan 29.
This report describes a 3-month-old Japanese boy with a diagnosis of isolated unilateral agenesis of the proximal right pulmonary artery with severe pulmonary hypertension. One-stage reconstruction of the right pulmonary artery was performed without cardiopulmonary bypass. The hilar right pulmonary artery and the distal main pulmonary artery were joined by anastomosis to an artificial ring graft. The boy's postoperative course was uneventful, and the pressure in the pulmonary artery was within the normal range. Although mild right pulmonary artery stenosis remained, the authors' therapeutic strategy may provide a clinically important option for isolated unilateral agenesis of the pulmonary artery.
本报告描述了一名3个月大的日本男婴，诊断为孤立性右侧近端肺动脉发育不全并伴有严重肺动脉高压。在非体外循环下进行了右肺动脉一期重建。通过吻合将肺门右肺动脉和远端主肺动脉与人工环形移植物相连。患儿术后病程顺利，肺动脉压力在正常范围内。尽管仍存在轻度右肺动脉狭窄，但作者的治疗策略可能为孤立性单侧肺动脉发育不全提供一种具有临床重要意义的选择。
