Cikrikcioglu M A, Erkal H, Hursitoglu M, Karadag A, Gundogan E, Kayacan S M, Tukek T
Vakif Gureba Training and Research Hospital, Fatih, Istanbul, Turkey.
Acta Gastroenterol Belg. 2010 Oct-Dec;73(4):521-6.
A 43-year old male patient with hyponatremic hypertensive syndrome was diagnosed as catastrophic primary antiphospholipid syndrome (PAPS). He subsequently developed hepatosplenomegaly. The patient also carried thrombophilia- and haemochromatosis-associated gene mutations. Further investigations upon persistence of splenomegaly indicated development of idiopathic portal hypertension.
一名患有低钠血症性高血压综合征的43岁男性患者被诊断为灾难性原发性抗磷脂综合征（PAPS）。随后他出现了肝脾肿大。该患者还携带与血栓形成倾向和血色素沉着症相关的基因突变。对持续性脾肿大进行的进一步检查表明出现了特发性门静脉高压。
