Kriet M, Fiqhi A, Bouya Y, Louaya S, Laktaoui A
Service d'Ophtalmologie, Hôpital Militaire Avicenne, Marrakech.
Bull Soc Belge Ophtalmol. 2010(316):43-7.
Sneddon's syndrome is a particular and rare entity that mostly affects young women and whose diagnosis is based on the coexistence of a cuteaneous livedo and a cerebrovascular ischemic attack. It had be considered as being an expression of an occlusive vasculitis or of antiphospholipid antibody syndrome. We report the case of a 20-year-old female, who had developed a left homonymous hemianopia after ischemic encephalopathy. Visual field examination confirmed the presence of a complete left homonymous hemianopia. Cerebral Magnetic Resonance Imaging revealed right occipital cerebrovascular ischemic lesions. Sneddon's syndrome diagnosis was considered on the presence of cutaneous livedo reticularis and associated cerebral ischemic events. With medical treatment, a small functional improvement could be noticed but without net improvement in the visual field defect.
斯内登综合征是一种特殊且罕见的病症,主要影响年轻女性,其诊断基于皮肤网状青斑和脑血管缺血性发作并存。它曾被认为是闭塞性血管炎或抗磷脂抗体综合征的一种表现形式。我们报告一例20岁女性病例,该患者在缺血性脑病后出现左侧同向性偏盲。视野检查证实存在完全性左侧同向性偏盲。脑部磁共振成像显示右侧枕叶脑血管缺血性病变。鉴于存在皮肤网状青斑及相关的脑部缺血事件,考虑诊断为斯内登综合征。经过药物治疗,可以观察到有轻微的功能改善,但视野缺损没有明显改善。