Hashmi Asra, Podgaetz Eitan, Richards Melanie L
Mayo Clinic, Rochester, Minnesota, USA; Dow University of Health Sciences, Karachi, Pakistan.
JSLS. 2010 Jul-Sep;14(3):426-30. doi: 10.4293/108680810X12924466007043.
Splenic tumors are rare. Malignant fibrous histiocytoma (MFH) of the spleen is one of the least common primary splenic tumors. Review of the literature shows that a laparoscopic resection has never been tried.
We discuss the case of a 76-year-old man with a 7-cm MFH in the spleen and present a review of splenic sarcomas.
The patient underwent a successful laparoscopic splenectomy; pathology revealed a rare undifferentiated pleomorphic sarcoma of the spleen. A review of the international literature identified 15 additional cases of primary splenic MFH. Survival was rarely longer than 15 months.
Malignant fibrous histiocytoma of the spleen is an exceedingly rare tumor with a poor prognosis. In experienced hands, laparoscopic splenectomy is a feasible operative choice for primary splenic sarcoma.
脾脏肿瘤较为罕见。脾脏恶性纤维组织细胞瘤（MFH）是最不常见的原发性脾脏肿瘤之一。文献回顾显示，从未尝试过腹腔镜切除术。
我们讨论了一名76岁男性脾脏有一个7厘米MFH的病例，并对脾脏肉瘤进行了综述。
患者成功接受了腹腔镜脾切除术；病理显示为罕见的脾脏未分化多形性肉瘤。对国际文献的回顾发现了另外15例原发性脾脏MFH病例。生存期很少超过15个月。
脾脏恶性纤维组织细胞瘤是一种极其罕见且预后不良的肿瘤。在经验丰富的医生手中，腹腔镜脾切除术是原发性脾脏肉瘤可行的手术选择。
