Akgüllü Cağdaş, Erdoğan Ercan, Akça Ozgür, Cevik Belma
Department of Cardiology, Aksaray State Hospital, Aksaray, Turkey.
Turk Kardiyol Dern Ars. 2011 Jan;39(1):68-71.
We present a 19-year-old asymptomatic female patient in whom isolated pulmonary supravalvular stenosis and pulmonary artery aneurysm were incidentally detected. On cardiologic examination, a systolic murmur was heard over the lungs, right axis deviation was seen on the electrocardiogram, and marked appearance of the pulmonary artery was noted on the chest X-ray. On transthoracic echocardiography, the pulmonary artery trunk was found to be wider than normal, and there were mild pulmonary and tricuspid regurgitation. Color Doppler examination showed a turbulent flow 2 cm distal to the pulmonary valve. Transesophageal echocardiography showed a supravalvular membranous structure and a proximal pulmonary artery aneurysm. The pulmonary artery trunk was measured as 40 mm at the widest part. Thoracic computed tomography revealed that the proximal pulmonary artery aneurysm was localized to the pulmonary artery trunk and measured 41 mm. As the patient was asymptomatic and there were no signs of aneurysmatic compression or a left-to-right shunt, and due to the presence of a relatively low gradient (16 mmHg) across the stenotic area, she was scheduled to regular radiologic control.
我们报告一例19岁无症状女性患者，其偶然发现孤立性肺动脉瓣上狭窄和肺动脉瘤。心脏检查时，肺部可闻及收缩期杂音，心电图显示电轴右偏，胸部X线片显示肺动脉明显增粗。经胸超声心动图检查发现肺动脉主干比正常宽，有轻度肺动脉瓣反流和三尖瓣反流。彩色多普勒检查显示肺动脉瓣远端2 cm处有湍流。经食管超声心动图显示瓣上膜性结构和近端肺动脉瘤。肺动脉主干最宽处测量为40 mm。胸部计算机断层扫描显示近端肺动脉瘤局限于肺动脉主干，大小为41 mm。由于患者无症状，无动脉瘤压迫或左向右分流迹象，且狭窄部位的压差相对较低（16 mmHg），她被安排定期进行影像学检查。
