Volpi L, Ricci G, Orsucci D, Alessi R, Bertolucci F, Piazza S, Simoncini C, Mancuso M, Siciliano G
Department of Neuroscience, Neurological Clinic, University of Pisa, Via Roma 67, 56126 Pisa, Italy.
Musculoskelet Surg. 2011 Aug;95(2):59-67. doi: 10.1007/s12306-011-0096-9. Epub 2011 Mar 4.
Metabolic myopathies are a clinically and etiologically heterogeneous group of disorders due to defects in muscular energy metabolism. They include glycogen storage diseases, fatty acid oxidation defects, and mitochondrial disorders. The typical manifestations of a metabolic myopathy are exercise-induced myalgias, exercise intolerance, and cramps. Evaluating subjects with such symptoms is not easy because of the frequent lack of clinical features. Exercise tests are, therefore, reliable screening tools. Here, we discuss the possible role of such exercise testing techniques in the diagnostic approach of a patient with suspected metabolic myopathy.
代谢性肌病是一组临床和病因学上异质性的疾病,归因于肌肉能量代谢缺陷。它们包括糖原贮积病、脂肪酸氧化缺陷和线粒体疾病。代谢性肌病的典型表现是运动诱发的肌痛、运动不耐受和痉挛。由于常常缺乏临床特征,评估有这些症状的受试者并不容易。因此,运动试验是可靠的筛查工具。在此,我们讨论此类运动试验技术在疑似代谢性肌病患者诊断方法中的可能作用。