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胸膜外间叶性软骨肉瘤:1例罕见病例报告

Extraskeletal mesenchymal chondrosarcoma of the pleura: report of a rare case.

作者信息

Jain Ayushi, Safaya Rajni, Jagan Chandramohan, Sharma S K

机构信息

Department of Pathology, All India Institute of Medical Sciences (AIIMS), New Delhi, India.

出版信息

Indian J Pathol Microbiol. 2011 Jan-Mar;54(1):144-6. doi: 10.4103/0377-4929.77374.

DOI:10.4103/0377-4929.77374
PMID:21393900
Abstract

Mesenchymal chondrosarcoma is a rare aggressive variant of chondrosarcoma that frequently occurs in extraskeletal location. A 28-year-old female presented with a history of dyspnea and fever and succumbed to her illness before a conclusive diagnosis was established. An autopsy performed revealed the presence of an extraskeletal mesenchymal chondrosarcoma (ESMC) involving the pleura. Only one case of ESMC of the pleura has been reported previously. Herein, we report the second case of ESMC of the pleura.

摘要

间叶性软骨肉瘤是软骨肉瘤的一种罕见侵袭性变体,常发生于骨骼外部位。一名28岁女性患者有呼吸困难和发热病史,在确诊前死亡。尸检发现存在累及胸膜的骨骼外间叶性软骨肉瘤(ESMC)。此前仅报道过1例胸膜ESMC。在此,我们报告第2例胸膜ESMC。

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