Komarlu Rukmini, Beerman Lee, Freeman David, Arora Gaurav
Department of Pediatric Cardiology, Children's Hospital of Pittsburgh of UPMC, Pittsburgh, Pennsylvania 15224, USA.
Pacing Clin Electrophysiol. 2012 Apr;35(4):e87-90. doi: 10.1111/j.1540-8159.2011.03040.x. Epub 2011 Mar 14.
This report describes a fetus presenting with intrauterine tachycardia and hydrops fetalis. Soon after birth the neonate was noted to be in torsades de pointes that responded dramatically to medical management. Long QT syndrome (LQTS) was diagnosed on electrocardiogram obtained soon after birth. The prognosis is poor when LQTS presents in utero or during the first week of life. However, our infant did well with medical management and has remained free of arrhythmias at follow-up.
本报告描述了一名患有宫内心动过速和胎儿水肿的胎儿。出生后不久，新生儿被发现患有尖端扭转型室速，经药物治疗后反应显著。出生后不久获得的心电图诊断为长QT综合征（LQTS）。当LQTS在子宫内或出生后第一周出现时，预后较差。然而，我们的婴儿经药物治疗后情况良好，随访期间一直没有心律失常。
