Aziz Peter F, Shah Maully J
Department of Pediatric Cardiology, Cleveland Clinic Lerner College of Medicine, The Cleveland Clinic Foundation, Cleveland, Ohio, USA.
Congenit Heart Dis. 2013 Nov-Dec;8(6):E165-7. doi: 10.1111/chd.12014. Epub 2012 Oct 18.
Long QT syndrome in the infant with 2:1 atrioventricular block is a malignant form of disease associated with frequent torsade de pointes in some cases. Those patients that do not respond to antiarrhythmic therapy are particularly challenging to manage. Ventricular pacing in this patient population has been shown to reduce arrhythmic events. We report a case of a newborn with frequent torsade de pointes requiring defibrillation and cardiopulmonary resuscitation with immediate shortening of the QTc interval with ventricular pacing and subsequent resolution of torsade de pointes.
患有2:1房室传导阻滞的婴儿长QT综合征是一种恶性疾病，在某些情况下与频发尖端扭转型室速相关。那些对抗心律失常治疗无反应的患者管理起来特别具有挑战性。在这一患者群体中，心室起搏已被证明可减少心律失常事件。我们报告一例新生儿频发尖端扭转型室速，需要除颤和心肺复苏，心室起搏后QTc间期立即缩短，随后尖端扭转型室速得以缓解。
