因进行性心脏病导致的 Emery-Dreifuss 肌营养不良症患者的心房瘫痪。

Atrial paralysis due to progression of cardiac disease in a patient with Emery-Dreifuss muscular dystrophy.

机构信息

Faculty of Health Studies, University of Humanities and Science, Kielce, Poland.

出版信息

Cardiol J. 2011;18(2):189-93.

Abstract

We present the progressive nature of the disease in a 26 year-old woman who had suffered from Emery-Dreifuss muscular dystrophy detected at the age of three. In 2002, at the age of 20, due to recurring presyncopal states accompanied by sinus bradycardia and atrioventricular block, she was implanted with a dual chamber pacing system. During testing of the pacing in 2008, permanent electrical atrial stand-still without atria stimulation were detected and the mode of heart stimulation was changed to VVIR.

摘要

我们呈现了一位 26 岁女性疾病进展的情况，她在三岁时被诊断患有 Emery-Dreifuss 肌营养不良症。2002 年，20 岁时，由于反复出现先兆晕厥伴有窦性心动过缓和房室传导阻滞，她被植入了双腔起搏系统。2008 年进行起搏测试时，发现心房出现永久性电静止而没有心房刺激，并将心脏刺激模式更改为 VVIR。