Gurioli C, Casoni G L, Gurioli C, Tomassetti S, Romagnoli M, Ravaglia C, Poletti V
Interventional Pulmonology Unit, Department of Thoracic Diseases, P.L. Pierantoni, G.B. Morgagni Hospital, Via Carlo Forlanini 34, 47100, Forlì, Italy.
Monaldi Arch Chest Dis. 2010 Dec;73(4):166-8. doi: 10.4081/monaldi.2010.287.
Dieulafoy's disease is a rare vascular malformation represented by an abnormally enlarged submucosal arterial vessel. This malformation is mostly found in gastrointestinal tract causing spontaneous bleeding although a few cases have been described in the bronchial tree. Recognizing Dieulafoy's malformation is crucial for the bronchoscopist in order to avoid biopsy that can lead to a massive hemoptysis, sometimes fatal. In this case report we show the clinical utility of endobronchial ultrasound (EBUS) in the evaluation of bronchial alteration suspicious for Dieulafoy's malformation.
迪厄拉富瓦病是一种罕见的血管畸形，其特征为黏膜下动脉血管异常增粗。这种畸形多见于胃肠道，可导致自发性出血，不过也有少数病例发生于支气管树。对于支气管镜检查医师而言，识别迪厄拉富瓦畸形至关重要，这样可避免活检引发大量咯血，有时甚至会致命。在本病例报告中，我们展示了支气管内超声（EBUS）在评估疑似迪厄拉富瓦畸形的支气管病变中的临床应用价值。
