Steiner Denise, Silva Fernanda Ayres de Morais e, Pessanha André César Antiori Freire, Bialeski Nediana, Feola Camila, Buzzoni Carla Arantes Bertolucci
University of Mogi das Cruzes, Sao Paulo, SP, Brazil.
An Bras Dermatol. 2011 Jan-Feb;86(1):165-6. doi: 10.1590/s0365-05962011000100032.
Becker nevus syndrome is the association of Becker's nevus with breast hypoplasia and other ipsilateral bone or muscle changes. It is considered to be a hormone-dependent disorder caused by a disturbance in the activity of the androgen receptor that appears to be increased in Becker's nevus, which may influence the development of associated lesions. We present a relevant case of this syndrome due to the rare systematization of the lesions in addition to the exuberant extracutaneous involvement in this case.
贝克尔痣综合征是指贝克尔痣与乳腺发育不全以及同侧其他骨骼或肌肉改变同时存在。它被认为是一种激素依赖性疾病，由雄激素受体活性紊乱引起，而雄激素受体活性在贝克尔痣中似乎有所增加，这可能影响相关病变的发展。由于该病例中病变罕见地系统化，且伴有广泛的皮肤外受累，我们在此呈现这一综合征的相关病例。
