Cine Nihat, Basaran Murat, Guzelmeric Fusun, Sunar Hasan
Department of Cardiovascular Surgery, Kosuyolu Heart and Research Hospital, Istanbul, Turkey.
Interact Cardiovasc Thorac Surg. 2011 Jun;12(6):1051-3. doi: 10.1510/icvts.2010.265082. Epub 2011 Mar 25.
Arterial tortuosity syndrome (ATS) is a rare connective tissue disease characterized by aneurysms and stenosis of large elastic arteries. In this case report, we present the case of an eight-year-old with ATS who underwent successful hemi-arch and ascending aortic replacement with tube graft.
动脉迂曲综合征(ATS)是一种罕见的结缔组织疾病,其特征为大弹性动脉的动脉瘤和狭窄。在本病例报告中,我们介绍了一名患有ATS的8岁患儿,其成功接受了半弓和升主动脉置换并使用了人工血管。