结缔组织病患者主动脉瘤的管理
Management of aortic aneurysms in patients with connective tissue disease.
作者信息
Schoenhoff F, Schmidli J, Czerny M, Carrel T P
机构信息
Department of Cardiovascular Surgery, University Hospital Berne, Berne, Switzerland.
出版信息
J Cardiovasc Surg (Torino). 2013 Feb;54(1 Suppl 1):125-34.
PMID:23443597
Abstract
Acute dissection and rupture of aortic aneurysms comprise for 1-2% of all deaths in developed countries. Dilation of the aorta is caused by several different mechanisms including inherited disorders of connective tissue. Recent reports estimate that 20% of patients presenting with thoracic aortic disease do have an underlying genetic basis of disease.
摘要
在发达国家，急性主动脉瘤夹层和破裂占所有死亡病例的1%-2%。主动脉扩张由多种不同机制引起，包括遗传性结缔组织疾病。最近的报告估计，20%出现胸主动脉疾病的患者确实有潜在的疾病遗传基础。
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