Vanhecke Thomas E, Decker Jeffrey, Leonowicz Nicholas, Chinnaiyan Kavitha M
Department of Cardiovascular Medicine, William Beaumont Hospital, Royal Oak, MI, USA.
Congenit Heart Dis. 2011 Nov-Dec;6(6):646-9. doi: 10.1111/j.1747-0803.2011.00489.x. Epub 2011 Mar 28.
Isolated left ventricular (LV) apical hypoplasia is a recently described congenital abnormality characterized by: (1) a truncated and spherical LV configuration with rightward bulging of the interventricular septum, (2) deficiency of the myocardium within the LV apex with adipose tissue infiltrating the apex, (3) origin of the papillary muscle in the flattened anterior apex, and (4) elongation of the right ventricle wrapping around the deficient LV apex. In this report, we demonstrate these characteristic features with cardiac magnetic resonance imaging and summarize the existing information on isolated LV apical hypoplasia.
孤立性左心室心尖发育不全是一种最近才被描述的先天性异常，其特征为：（1）左心室呈截断的球形形态，室间隔向右膨出；（2）左心室心尖部心肌缺损，脂肪组织浸润心尖；（3）乳头肌起源于扁平的前心尖；（4）右心室延长并包裹发育不全的左心室心尖。在本报告中，我们通过心脏磁共振成像展示了这些特征，并总结了关于孤立性左心室心尖发育不全的现有信息。
