Fernandez-Valls M, Srichai M B, Stillman A E, White R D
Department of Radiology (Section of Cardiovascular Imaging), Cleveland Clinic Foundation, Cleveland, Ohio 44195, USA.
Heart. 2004 May;90(5):552-5. doi: 10.1136/hrt.2003.010637.
To describe cardiac tomography findings of an apparently new, presumably congenital, left ventricular (LV) abnormality noted consistently in three patients.
Three patients presenting with non-specific symptoms including fatigue, shortness of breath, or chest discomfort were evaluated with cardiac tomography for cardiac structure and function.
Findings from the three patients were very similar: a truncated and spherical LV with abnormal diastolic and systolic function, invagination of fatty material into the myocardium of the defective LV apex, origin of a complex papillary network in the anteroapical LV, and an elongated right ventricle wrapping around the deficient apex.
Isolated LV apical hypoplasia is a unique, presumably congenital, cardiac anomaly that is an important condition to recognise.
描述在三名患者中持续发现的一种明显新的、可能为先天性的左心室（LV）异常的心脏断层扫描结果。
对三名出现包括疲劳、呼吸急促或胸部不适等非特异性症状的患者进行心脏断层扫描以评估心脏结构和功能。
三名患者的检查结果非常相似：左心室呈截断状且球形，舒张和收缩功能异常，脂肪物质内陷至有缺陷的左心室心尖心肌，复杂乳头肌网络起源于左心室前心尖，以及伸长的右心室环绕缺损的心尖。
孤立性左心室心尖发育不全是一种独特的、可能为先天性的心脏异常，是一种需要识别的重要病症。
