红斑狼疮伴 Kluver-Bucy 综合征 1 例

Kluver-Bucy syndrome in one case with systemic lupus erythematosus.

机构信息

Department of Neurology, Kaohsiung Medical University Hospital, Kaohsiung, Taiwan.

出版信息

Kaohsiung J Med Sci. 2011 Apr;27(4):159-62. doi: 10.1016/j.kjms.2010.12.011. Epub 2011 Feb 17.

DOI:10.1016/j.kjms.2010.12.011

Abstract

Kluver-Bucy syndrome (KBS) is a collection of neuropsychiatric symptoms, including visual agnosia (prosopagnosia), hypermetamorphosis, placidity, hypersexuality, and hyperorality. Although neuropsychiatric manifestation is prevalent in cases with systemic lupus erythematosus (SLE), only one literature reported a case with SLE that had KBS previously. In this article, a 37-year-old woman with SLE who developed KBS and other neuropsychiatric symptoms is presented. Brain imaging proved the relevant structural lesion. The possible explanation of pathogenesis of KBS in SLE is discussed.

摘要

克莱-伯二氏综合征（KBS）是一组神经精神症状，包括视觉失认症（面容失认症）、过度变形、温顺、性欲亢进和过度咀嚼。尽管神经精神表现常见于系统性红斑狼疮（SLE）病例中，但仅有一篇文献曾报道过一例 SLE 患者合并 KBS。本文报道了一例 37 岁 SLE 女性患者，其出现 KBS 及其他神经精神症状。脑影像学检查证实了相关的结构性病变。讨论了 SLE 中 KBS 发病机制的可能解释。