血管滤泡性淋巴结增生症：8 岁男孩门静脉肿块的罕见诊断。

Castleman disease: an unusual diagnosis of a portal mass in an 8-year-old boy.

机构信息

Department of Pediatric Surgery, Hacettepe University Faculty of Medicine, Ankara 06100, Turkey.

Department of Pediatric Pathology, Hacettepe University Faculty of Medicine, Ankara 06100, Turkey.

出版信息

J Pediatr Surg. 2011 Apr;46(4):e9-e11. doi: 10.1016/j.jpedsurg.2010.12.005.

DOI:10.1016/j.jpedsurg.2010.12.005

PMID:21496526

Abstract

An 8-year-old boy presented with a mass located in the portal hilum and hepatosplenomegaly, and the presumed initial diagnosis was lymphoma. The pathology result was Castleman disease of hyaline vascular type. Castleman disease is an unusual diagnosis that should be kept in mind in the differential diagnosis of portal masses. In the case of solitary lesions, total excision can be curative.

摘要

一位 8 岁男孩因门静脉汇区肿块和肝脾肿大就诊，初步诊断为淋巴瘤。病理结果为透明血管型 Castleman 病。Castleman 病是一种不常见的诊断，在门静脉肿块的鉴别诊断中应予以考虑。对于单发病变，完全切除可达到治愈。