Patwardhan S, Shyam A K, Sancheti P, Arora P, Nagda T, Naik P
Sancheti Institute for Orthopaedics and Rehabilitation, 16 Shivaji Nagar, Pune, Maharashtra State 411005, India.
J Bone Joint Surg Br. 2011 Jun;93(6):828-32. doi: 10.1302/0301-620X.93B6.26232.
Adult presentation of neglected congenital muscular torticollis is rare. We report 12 patients with this condition who underwent a modified Ferkel's release comprising a bipolar release of sternocleidomastoid with Z-lengthening. They had a mean age of 24 years (17 to 31) and were followed up for a minimum of two years. Post-operatively a cervical collar was applied for three weeks with intermittent supervised active assisted exercises for six weeks. Outcome was assessed using a modified Lee score and a Cheng and Tang score. The mean pre-operative rotational deficit was 8.25° (0° to 15°) and mean lateral flexion deficit was 20.42° (15° to 30°), which improved after treatment to a mean of 1.67° (0° to 5°) and 7.0° (4° to 14°) after treatment, respectively. According to the modified Lee scoring system, six patients had excellent results, two had good results and four had fair results, and using the Cheng and Tang score, eight patients had excellent results and four had good results. Surgical management of adult patients with neglected congenital muscular torticollis using a modified Ferkel's bipolar release gives excellent results. The range of neck movement and head tilt improved in all 12 patients and cosmesis improved in 11, despite the long-standing nature of the deformity.
成人期出现的先天性肌性斜颈较为罕见。我们报告了12例患有这种疾病的患者,他们接受了改良的费克尔松解术,包括胸锁乳突肌的双极松解及Z形延长术。他们的平均年龄为24岁(17至31岁),且至少随访了两年。术后使用颈托三周,并进行为期六周的间歇性监督下的主动辅助锻炼。使用改良的李评分和程氏及唐氏评分对结果进行评估。术前平均旋转受限为8.25°(0°至15°),平均侧屈受限为20.42°(15°至30°),治疗后分别改善至平均1.67°(0°至5°)和7.0°(4°至14°)。根据改良的李评分系统,6例患者结果为优,2例为良,4例为中;使用程氏及唐氏评分,8例患者结果为优,4例为良。采用改良的费克尔双极松解术对成人期先天性肌性斜颈患者进行手术治疗,效果极佳。尽管畸形存在时间较长,但所有12例患者的颈部活动范围和头部倾斜度均有所改善,11例患者的外观也得到改善。