Division of Reproductive Endocrinology and Infertility, Department of Obstetrics and Gynecology, Brigham and Women's Hospital, Boston, Massachusetts, USA.
Fertil Steril. 2011 Jul;96(1):e39-41. doi: 10.1016/j.fertnstert.2011.05.013. Epub 2011 May 24.
To describe an unusual case of obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome with a single uterus.
Case report.
Major academic medical center.
PATIENT(S): A 12-year-old girl with OHVIRA syndrome.
INTERVENTION(S): None.
MAIN OUTCOME MEASURE(S): None.
RESULT(S): A 12-year-old girl presented with presumed OHVIRA syndrome and had surgical correction of the obstructed hemivagina. Two years later she presented with increasing pelvic pain and underwent laparoscopy for presumed endometriosis. A single uterus with a broad flat fundus was found as well as endometriosis.
CONCLUSION(S): OHVIRA syndrome is typically associated with a didelphys uterus with two cervices and two vaginas, one of which is obstructed. The obstruction usually occurs on the same side as the renal anomaly. We report a rare congenital anomaly of the female reproductive tract: OHVIRA syndrome with a single uterus. From a fertility standpoint, cases of a single uterus with two cervices are managed differently than two uteri with two cervices. Healthcare providers managing complex reproductive tract anomalies should be aware of this potential variant.
描述一例单侧隐阴道和同侧肾发育不全（OHVIRA）综合征伴单子宫的罕见病例。
病例报告。
主要学术医疗中心。
12 岁 OHVIRA 综合征女孩。
无。
无。
一名 12 岁女孩因疑似 OHVIRA 综合征接受了单侧隐阴道梗阻的手术矫正。两年后，她因盆腔疼痛加重行腹腔镜检查，诊断为子宫内膜异位症。发现单子宫，宫底宽而扁，同时患有子宫内膜异位症。
OHVIRA 综合征通常与双子宫伴双宫颈和双阴道相关，其中一个阴道梗阻。梗阻通常发生在同侧肾发育不全侧。我们报告了一种罕见的女性生殖道先天性异常：OHVIRA 综合征伴单子宫。从生育角度来看，单子宫伴双宫颈的病例与双子宫伴双宫颈的病例处理方式不同。管理复杂生殖道异常的医疗保健提供者应注意到这种潜在的变异。
