Fujiwara Y, Abe Y, Kuyama M, Arata J, Yoshino T, Akagi T, Miyoshi K
Department of Dermatology, Okayama University Medical School, Japan.
Arch Dermatol. 1990 Jun;126(6):801-4.
A 68-year-old woman had a peculiar clinical course of cutaneous lymphoma. She first developed nonpuritic erythematous macules with fine scales followed by development of erythematous infiltrated plaques. The clinical course could be interpreted as that of mycosis fungoides. Histologically, the lesions showed pagetoid infiltration of atypical lymphoid cells. Suddenly, with high fever, numerous purpuric, ulcerated, or crusted plaques with underlying infiltration or nodules began to appear on most areas of the patient's body. Biopsy specimens of the lesions revealed angiocentric and angiodestructive infiltration by neoplastic T cells and marked epidermotropism of these cells. These atypical cells immunohistochemically had CD8+ surface phenotype. The patient died of respiratory insufficiency due to acute pulmonary infiltration. Autopsy demonstrated angiocentric and angiodestructive lymphomatous infiltration in the lung.
一名68岁女性患有一种特殊病程的皮肤淋巴瘤。她最初出现了带有细鳞屑的非瘙痒性红斑性斑疹,随后发展为红斑浸润性斑块。临床病程可解释为蕈样肉芽肿。组织学上,病变显示非典型淋巴细胞的派杰样浸润。突然,患者身体大部分区域开始出现高热,伴有大量紫癜性、溃疡或结痂的斑块,伴有深部浸润或结节。病变的活检标本显示肿瘤性T细胞呈血管中心性和血管破坏性浸润,且这些细胞有明显的亲表皮性。这些非典型细胞免疫组化显示具有CD8 +表面表型。患者因急性肺部浸润导致呼吸功能不全死亡。尸检显示肺部有血管中心性和血管破坏性淋巴瘤浸润。