• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

A harmonized classification system for FTLD-TDP pathology.

作者信息

Mackenzie Ian R A, Neumann Manuela, Baborie Atik, Sampathu Deepak M, Du Plessis Daniel, Jaros Evelyn, Perry Robert H, Trojanowski John Q, Mann David M A, Lee Virginia M Y

出版信息

Acta Neuropathol. 2011 Jul;122(1):111-3. doi: 10.1007/s00401-011-0845-8. Epub 2011 Jun 5.

DOI:10.1007/s00401-011-0845-8
PMID:21644037
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3285143/
Abstract
摘要

相似文献

1
A harmonized classification system for FTLD-TDP pathology.额颞叶痴呆-嗜银颗粒蛋白病(FTLD-TDP)病理学的统一分类系统。
Acta Neuropathol. 2011 Jul;122(1):111-3. doi: 10.1007/s00401-011-0845-8. Epub 2011 Jun 5.
2
Pathological heterogeneity of frontotemporal lobar degeneration with ubiquitin-positive inclusions delineated by ubiquitin immunohistochemistry and novel monoclonal antibodies.通过泛素免疫组织化学和新型单克隆抗体描绘的伴有泛素阳性包涵体的额颞叶变性的病理异质性
Am J Pathol. 2006 Oct;169(4):1343-52. doi: 10.2353/ajpath.2006.060438.
3
TDP-43-positive white matter pathology in frontotemporal lobar degeneration with ubiquitin-positive inclusions.伴有泛素阳性包涵体的额颞叶变性中的TDP - 43阳性白质病变
J Neuropathol Exp Neurol. 2007 Mar;66(3):177-83. doi: 10.1097/01.jnen.0000248554.45456.58.
4
Atypical frontotemporal lobar degeneration with ubiquitin-positive, TDP-43-negative neuronal inclusions.伴有泛素阳性、TDP-43阴性神经元包涵体的非典型额颞叶变性。
Brain. 2008 May;131(Pt 5):1282-93. doi: 10.1093/brain/awn061. Epub 2008 Mar 24.
5
Clinicopathological characterization of Pick's disease versus frontotemporal lobar degeneration with ubiquitin/TDP-43-positive inclusions.皮克病与伴有泛素/TDP-43阳性包涵体的额颞叶痴呆的临床病理特征
Acta Neuropathol. 2009 Apr;117(4):429-44. doi: 10.1007/s00401-009-0493-4. Epub 2009 Feb 5.
6
Histopathological changes underlying frontotemporal lobar degeneration with clinicopathological correlation.伴临床病理相关性的额颞叶痴呆的组织病理学改变
Acta Neuropathol. 2005 Nov;110(5):501-12. doi: 10.1007/s00401-005-1079-4. Epub 2005 Oct 13.
7
Neurofilament inclusion body disease: a new proteinopathy?神经丝包涵体病:一种新的蛋白病?
Brain. 2003 Oct;126(Pt 10):2291-303. doi: 10.1093/brain/awg231. Epub 2003 Jul 22.
8
Frontotemporal lobar degeneration and ubiquitin immunohistochemistry.额颞叶痴呆与泛素免疫组化
Neuropathol Appl Neurobiol. 2004 Aug;30(4):369-73. doi: 10.1111/j.1365-2990.2003.00545.x.
9
TDP-43-negative FTLD-U is a significant new clinico-pathological subtype of FTLD.TDP-43阴性的额颞叶痴呆-泛素阳性包含体病是额颞叶痴呆一种重要的新临床病理亚型。
Acta Neuropathol. 2008 Aug;116(2):147-57. doi: 10.1007/s00401-008-0395-x. Epub 2008 Jun 7.
10
TAR DNA-binding protein 43 immunohistochemistry reveals extensive neuritic pathology in FTLD-U: a midwest-southwest consortium for FTLD study.TAR DNA结合蛋白43免疫组化显示额颞叶痴呆-泛素阳性型(FTLD-U)存在广泛的神经突病变:一个用于FTLD研究的中西部-西南部联盟。
J Neuropathol Exp Neurol. 2008 Apr;67(4):271-9. doi: 10.1097/NEN.0b013e31816a12a6.

引用本文的文献

1
Differences and overlaps in TDP-43 pathology of 'pure' LATE-NC compared to LATE-NC coexisting with Alzheimer's disease.与阿尔茨海默病共存的晚发性神经认知障碍(LATE-NC)相比,“单纯”晚发性神经认知障碍(LATE-NC)的TDP-43病理学差异与重叠。
Acta Neuropathol. 2025 Sep 15;150(1):28. doi: 10.1007/s00401-025-02929-9.
2
Two-step detection of Lewy body pathology via smell-function testing and CSF α-synuclein seed amplification.通过嗅觉功能测试和脑脊液α-突触核蛋白种子扩增两步检测路易体病理。
Nat Commun. 2025 Aug 5;16(1):7182. doi: 10.1038/s41467-025-62458-7.
3
Spatial and Temporal Progression of Neurodegeneration in Confirmed and Suspected TDP-43 Type C Pathology.确诊和疑似TDP - 43 C型病理中神经退行性变的空间和时间进展
Imaging Neurosci (Camb). 2025;3. doi: 10.1162/imag.a.83. Epub 2025 Jul 16.
4
Corticobasal degeneration preceded by cognitive impairment and apathy: An autopsy case report.以认知障碍和淡漠为前驱症状的皮质基底节变性:一例尸检病例报告。
PCN Rep. 2025 Aug 3;4(3):e70174. doi: 10.1002/pcn5.70174. eCollection 2025 Sep.
5
Accelerating biomedical discoveries in brain health through transformative neuropathology of aging and neurodegeneration.通过衰老和神经退行性变的变革性神经病理学加速脑健康方面的生物医学发现。
Neuron. 2025 Jul 15. doi: 10.1016/j.neuron.2025.06.014.
6
Frontotemporal Lobar degeneration with TDP-43 presenting as progressive supranuclear palsy syndrome.伴有TDP-43的额颞叶变性表现为进行性核上性麻痹综合征。
Acta Neuropathol Commun. 2025 Jul 9;13(1):151. doi: 10.1186/s40478-025-02058-0.
7
Reduction of sphingomyelinase activity associated with progranulin deficiency and frontotemporal dementia.与原颗粒蛋白缺乏和额颞叶痴呆相关的鞘磷脂酶活性降低。
Neurobiol Dis. 2025 Sep;213:107024. doi: 10.1016/j.nbd.2025.107024. Epub 2025 Jul 7.
8
Methylome analysis of FTLD patients with TDP-43 pathology identifies epigenetic signatures specific to pathological subtypes.对患有TDP-43病理学的额颞叶痴呆(FTLD)患者进行甲基化组分析,确定了特定于病理亚型的表观遗传特征。
Mol Neurodegener. 2025 Jul 6;20(1):80. doi: 10.1186/s13024-025-00869-2.
9
Analysis of short tandem repeats linked to polyglutamine diseases from whole-genome sequencing reveals intermediate alleles of associated with an early disease onset in carriers.通过全基因组测序分析与多聚谷氨酰胺疾病相关的短串联重复序列,发现与携带者疾病早发相关的中间等位基因。
Brain Commun. 2025 Jun 4;7(3):fcaf220. doi: 10.1093/braincomms/fcaf220. eCollection 2025.
10
The mechanisms underlying TDP-43-associated neurodegeneration in Alzheimer's disease and related dementias.阿尔茨海默病及相关痴呆中与TDP-43相关的神经退行性变的潜在机制。
Mol Psychiatry. 2025 Jun 25. doi: 10.1038/s41380-025-03089-8.

本文引用的文献

1
Evaluation of subcortical pathology and clinical correlations in FTLD-U subtypes.额颞叶痴呆-泛素阳性型(FTLD-U)亚型的皮质下病理及临床相关性评估
Acta Neuropathol. 2009 Sep;118(3):349-58. doi: 10.1007/s00401-009-0547-7. Epub 2009 May 20.
2
Clinical and pathological continuum of multisystem TDP-43 proteinopathies.多系统TDP-43蛋白病的临床与病理连续谱
Arch Neurol. 2009 Feb;66(2):180-9. doi: 10.1001/archneurol.2008.558.
3
Nomenclature for neuropathologic subtypes of frontotemporal lobar degeneration: consensus recommendations.额颞叶变性神经病理学亚型的命名:共识推荐
Acta Neuropathol. 2009 Jan;117(1):15-8. doi: 10.1007/s00401-008-0460-5. Epub 2008 Nov 18.
4
TDP-43 immunoreactivity in neurodegenerative disorders: disease versus mechanism specificity.神经退行性疾病中的TDP-43免疫反应性:疾病与机制特异性
Acta Neuropathol. 2008 Jan;115(1):147-9. doi: 10.1007/s00401-007-0323-5. Epub 2007 Nov 23.
5
TDP-43 in familial and sporadic frontotemporal lobar degeneration with ubiquitin inclusions.伴有泛素包涵体的家族性和散发性额颞叶痴呆中的TDP-43
Am J Pathol. 2007 Jul;171(1):227-40. doi: 10.2353/ajpath.2007.070182.
6
TDP-43 in the ubiquitin pathology of frontotemporal dementia with VCP gene mutations.VCP基因突变的额颞叶痴呆泛素病理学中的TDP-43
J Neuropathol Exp Neurol. 2007 Feb;66(2):152-7. doi: 10.1097/nen.0b013e31803020b9.
7
Ubiquitinated pathological lesions in frontotemporal lobar degeneration contain the TAR DNA-binding protein, TDP-43.额颞叶变性中的泛素化病理病变包含TAR DNA结合蛋白TDP-43。
Acta Neuropathol. 2007 May;113(5):521-33. doi: 10.1007/s00401-006-0189-y. Epub 2007 Jan 12.
8
Ubiquitinated TDP-43 in frontotemporal lobar degeneration and amyotrophic lateral sclerosis.额颞叶痴呆和肌萎缩侧索硬化症中泛素化的TDP-43
Science. 2006 Oct 6;314(5796):130-3. doi: 10.1126/science.1134108.
9
Heterogeneity of ubiquitin pathology in frontotemporal lobar degeneration: classification and relation to clinical phenotype.额颞叶变性中泛素病理学的异质性:分类及其与临床表型的关系。
Acta Neuropathol. 2006 Nov;112(5):539-49. doi: 10.1007/s00401-006-0138-9. Epub 2006 Sep 26.
10
Pathological heterogeneity of frontotemporal lobar degeneration with ubiquitin-positive inclusions delineated by ubiquitin immunohistochemistry and novel monoclonal antibodies.通过泛素免疫组织化学和新型单克隆抗体描绘的伴有泛素阳性包涵体的额颞叶变性的病理异质性
Am J Pathol. 2006 Oct;169(4):1343-52. doi: 10.2353/ajpath.2006.060438.