Pathology Service, Massachusetts General Hospital (MGH), Boston, MA, USA.
Am J Transplant. 2011 Jul;11(7):1464-77. doi: 10.1111/j.1600-6143.2011.03572.x. Epub 2011 Jun 10.
An idiopathic capillary leak syndrome ('engraftment syndrome') often occurs in recipients of hematopoietic cells, manifested clinically by transient azotemia and sometimes fever and fluid retention. Here, we report the renal pathology in 10 recipients of combined bone marrow and kidney allografts. Nine developed graft dysfunction on day 10-16 and renal biopsies showed marked acute tubular injury, with interstitial edema, hemorrhage and capillary congestion, with little or no interstitial infiltrate (≤10%) and marked glomerular and peritubular capillary (PTC) endothelial injury and loss by electron microscopy. Two had transient arterial endothelial inflammation; and 2 had C4d deposition. The cells in capillaries were primarily CD68(+) MPO(+) mononuclear cells and CD3(+) CD8(+) T cells, the latter with a high proliferative index (Ki67(+) ). B cells (CD20(+) ) and CD4(+) T cells were not detectable, and NK cells were rare. XY FISH showed that CD45(+) cells in PTCs were of recipient origin. Optimal treatment remains to be defined; two recovered without additional therapy, six were treated with anti-rejection regimens. Except for one patient, who later developed thrombotic microangiopathy and one with acute humoral rejection, all fully recovered within 2-4 weeks. Graft endothelium is the primary target of this process, attributable to as yet obscure mechanisms, arising during leukocyte recovery.
特发性毛细血管渗漏综合征(“植入综合征”)常发生于造血细胞移植受者,临床上表现为短暂性氮质血症,有时伴有发热和体液潴留。本研究报道了 10 例骨髓和肾联合移植受者的肾脏病理。9 例受者于移植后第 10-16 天发生移植物功能障碍,肾活检显示明显的急性肾小管损伤,伴有间质水肿、出血和毛细血管淤血,间质浸润(≤10%)较少或几乎没有,且电子显微镜下肾小球和肾小管周围毛细血管(PTC)内皮损伤和丢失明显。2 例有短暂性动脉内皮炎症;2 例有 C4d 沉积。毛细血管中的细胞主要为 CD68(+) MPO(+)单核细胞和 CD3(+) CD8(+) T 细胞,后者有较高的增殖指数(Ki67(+))。B 细胞(CD20(+))和 CD4(+) T 细胞不可检测,NK 细胞罕见。XY FISH 显示 PTC 中的 CD45(+)细胞来源于受者。最佳治疗方法仍有待确定;2 例未经额外治疗而恢复,6 例接受了抗排斥治疗。除 1 例患者后来发生血栓性微血管病和 1 例发生急性体液排斥反应外,所有患者均在 2-4 周内完全恢复。移植物内皮是该过程的主要靶标,其发病机制尚不清楚,可能与白细胞恢复过程中的某些机制有关。