Roberts Tina, Stephen Lawrence, Scott Chris, Urban M, Sudi Stephen, Beighton Peter
Faculty of Dentistry, University of the Western Cape, Cape Town, South Africa.
Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 2011 Jul;112(1):11-8. doi: 10.1016/j.tripleo.2011.03.015.
Fibrodysplasia ossificans progressiva (FOP) is a severe genetic disorder in which progressive ossification of subcutaneous tissues leads to immobility and profound physical handicap. Dental management of affected persons may be constrained by impaired mobility of the temporomandibular joints. Equally, the traumatic aspects of dental intervention can exacerbate the ossification process. In the later stages of the disorder, thoracic immobility impairs pulmonary ventilation and compromises dental anesthesia. We have undertaken dental appraisal and treatment of 5 South Africans with FOP, with ages ranging from 2 to 52 years. The age relationship of the manifestations of FOP was apparent in these persons, as were the dental problems that emerged. These dental observations illustrate the importance of accurate diagnosis and the awareness of potential complications that may be encountered in dental management. Our observations are presented and discussed in this article.
进行性骨化性纤维发育不良(FOP)是一种严重的遗传性疾病,皮下组织的进行性骨化会导致活动受限和严重的身体残疾。受影响者的牙科治疗可能会因颞下颌关节活动受限而受到限制。同样,牙科干预的创伤性方面会加剧骨化过程。在该疾病的后期,胸廓活动受限会损害肺通气并影响牙科麻醉。我们对5名年龄在2至52岁之间的南非FOP患者进行了牙科评估和治疗。FOP表现的年龄关系在这些患者中很明显,出现的牙科问题也是如此。这些牙科观察结果说明了准确诊断的重要性以及对牙科治疗中可能遇到的潜在并发症的认识。本文将呈现并讨论我们的观察结果。