Nussbaum B L, O'Hara I, Kaplan F S
Children's Hospital of Philadelphia, USA.
ASDC J Dent Child. 1996 Nov-Dec;63(6):448-50.
Fibrodysplasia ossificans progressiva (FOP) is a rare heritable disorder of progressive heterotopic ossification leading to joint ankylosis throughout the body. Permanent ankylosis of the jaw may be precipitated by minimal soft tissue trauma, a potentially devastating complication following routine dental care during childhood. Assiduous precautions are necessary in administering dental care to children who have FOP as exemplified in this case report. Routine dental prophylaxis is also necessary in order to minimize the need for invasive procedures.
进行性骨化性纤维发育不良(FOP)是一种罕见的遗传性疾病,会导致全身进行性异位骨化,进而引起关节强直。轻微的软组织创伤可能会导致颌骨永久性强直,这是儿童期常规牙科护理后可能出现的一种潜在的毁灭性并发症。正如本病例报告所示,在为患有FOP的儿童提供牙科护理时,必须采取严格的预防措施。为尽量减少侵入性操作的必要性,常规牙齿预防措施也是必要的。