Borges-Cancel William, Calderón Rafael E
Section of Cardiology, Department of Medicine, School of Medicine, University of Puerto Rico Medical Sciences Campus, San Juan, Puerto Rico.
P R Health Sci J. 2011 Jun;30(2):84-6.
Left ventricular non-compaction cardiomyopathy (LVNC) is a rare disorder characterized by a thick myocardial wall with two distinct layers consisting of compacted and noncompacted myocardium. The major clinical manifestations of LVNC have been described as heart failure, cardiac arrhythmias, and cardioembolic events. In this report we present a case of a young woman with LVNC who presented with aborted sudden cardiac death. This is the second case of LVNC reported in Puerto Rico, but the first presenting with this complication. Recent advances in the field of cardiology allow the identification and diagnosis of this disease; thus, preventive and treatment strategies could be established for this potentially life-threatening condition. LVNC has to be considered in young patients presenting with sudden cardiac death.
左心室致密化不全心肌病（LVNC）是一种罕见的疾病，其特征是心肌壁增厚，由致密心肌和非致密心肌组成两个不同的层。LVNC的主要临床表现为心力衰竭、心律失常和心脏栓塞事件。在本报告中，我们介绍了一例患有LVNC的年轻女性病例，该患者出现了心脏骤停。这是波多黎各报道的第二例LVNC病例，但第一例出现了这种并发症。心脏病学领域的最新进展使得能够识别和诊断这种疾病；因此，可以为这种潜在的危及生命的疾病制定预防和治疗策略。对于出现心脏骤停的年轻患者，必须考虑LVNC。
