Department of Pediatric Surgery, Shengjing Hospital Affiliated to China Medical University, Shenyang City 110004, China.
J Pediatr Surg. 2011 Jun;46(6):1284-7. doi: 10.1016/j.jpedsurg.2011.03.016.
We report a 5-year-old boy with a cystic lymphatic malformation (LM) of bladder, and the imaging characteristics of the lesion are reported. Cystic LM of the urinary system is rare, and a location in the bladder is extremely rare. The exact mechanism of the lesion that occurs in bladder is unknown. This case is different from the 3 cases reported before, for it is only presented with a palpable pelvic mass and the lesion did not penetrate full thickness of bladder. Although imaging examinations are helpful in the definition of cystic LMs, no characteristic findings are available to diagnose a cystic LM of the bladder before surgery. The diagnosis is always made after surgical intervention. Surgical excision is ideal, and an extensive operation is not warranted because the lesion is benign. Once excised completely, the prognosis of the disease is good.
我们报告了一例 5 岁男孩的膀胱囊性淋巴管畸形（LM），并报道了病变的影像学特征。泌尿系统囊性 LM 较为罕见，发生在膀胱的位置极其罕见。病变发生在膀胱的确切机制尚不清楚。该病例与之前报告的 3 例不同，因为它仅表现为可触及的盆腔肿块，且病变未穿透膀胱全层。虽然影像学检查有助于明确囊性 LM，但在手术前没有特征性发现可诊断膀胱囊性 LM。诊断总是在手术干预后做出。手术切除是理想的，因为病变是良性的，所以不需要广泛的手术。一旦完全切除，疾病的预后良好。
