Esthesioneuroblastoma (ENB) is a rare, malignant neoplasm arising from the olfactory epithelial cells, with only approximately 100 pediatric cases being reported in the literature since its original description in 1924. As a result of its origin high in the nasal cavity, most patients have non-specific symptoms, precluding early diagnosis and leading to the development of locally advanced disease that usually has been found to involve the orbital cavity, paranasal sinuses, and anterior cranial fossa in children. The purpose of this paper was to report a rare case of pediatric esthesioneuroblastoma diagnosed following the patient's dental complaints, wherein local invasion of the tumor into the maxillofacial region was noticed before its extension into other vital structures.