Sobani Zain A, Junaid Montasir, Khan Mumtaz J
Medical College, Aga Khan University, Stadium Road, Karachi, Pakistan.
J Med Case Rep. 2011 Jun 27;5:244. doi: 10.1186/1752-1947-5-244.
Aggressive fibromatosis is a benign tumor, thought to arise from deep musculoaponeurotic structures, rarely found in the head or neck. However, when it does occur in the head and neck region, it tends to be more aggressive and associated with significant morbidity, which may be attributed to the vital vascular, neurological or anatomical structures in close proximity.
We report the case of a 39-year-old Pakistani man who presented with a two-month history of a lump on the right side of his neck. The mass was excised and histopathological analysis revealed a case of aggressive fibromatosis.
Due to the rarity of the condition no guidelines are available on the indications and extent of each modality. Due to its aggressive behavior and tendency to invade local structures and recur, a multi-modality management strategy is usually employed. On the basis of this case, we suggest that aggressive surgery is a viable management option and may be successfully used as a single modality treatment.
侵袭性纤维瘤病是一种良性肿瘤,被认为起源于深部肌筋膜结构,在头颈部很少见。然而,当它确实发生在头颈部区域时,往往更具侵袭性,并伴有严重的发病率,这可能归因于附近重要的血管、神经或解剖结构。
我们报告一例39岁的巴基斯坦男性病例,该患者右侧颈部有肿块,病史两个月。肿块被切除,组织病理学分析显示为侵袭性纤维瘤病。
由于这种疾病罕见,目前尚无关于每种治疗方式的适应症和范围的指南。由于其侵袭性行为以及侵犯局部结构和复发的倾向,通常采用多模式管理策略。基于该病例,我们建议积极的手术是一种可行的管理选择,并且可以成功地用作单一模式治疗。