Kent B D, Sulaiman I, Akasheh N B, Nadarajan P, Moloney E, Lane S J
Department of Respiratory Medicine, Pulmonary and Sleep Disorders Unit, St Vincent's University Hospital, Dublin 4.
Ir Med J. 2011 May;104(5):152-3.
We present the case of a 54-year old woman referred to our service with an unusual presentation of an under-diagnosed condition. A life-long non-smoker, she was referred to respiratory services by our emergency department with a left sided pneumothorax, progressive dyspnoea on exertion, and recurrent chest infections. Subsequent investigation yielded findings consistent with Mounier-Kuhn syndrome (Tracheobronchomegaly), a condition characterised by marked dilatation of the proximal airways, recurrent chest infection, and consequent emphysema and bronchiectasis. Although rarely diagnosed, some degree of Mounier-Kuhn syndrome may occur in up to 1 in 500 adults.
我们报告了一例54岁女性患者,她因一种诊断不足的疾病的不寻常表现前来我们科室就诊。她终生不吸烟,因左侧气胸、运动性进行性呼吸困难和反复肺部感染被我院急诊科转诊至呼吸科。后续检查结果与穆尼尔-库恩综合征(气管支气管巨大症)相符,该疾病的特征是近端气道明显扩张、反复肺部感染以及随之而来的肺气肿和支气管扩张。尽管很少被诊断出来,但高达五百分之一的成年人可能会出现某种程度的穆尼尔-库恩综合征。