Sahu Sandeep, Lata Indu, Singh Surendra, Kumar Mukesh
Department of Anaesthesiology, Lucknow, UP, India.
J Emerg Trauma Shock. 2011 Apr;4(2):292-8. doi: 10.4103/0974-2700.82225.
The World Federation of Hemophilia estimates that more than 350,000 people globally have a form of the disease. Hemophilia A is a bleeding disorder that has a spectrum of manifestations ranging from persistent bleeding after minor trauma to spontaneous hemorrhage. We report a case of a male patient with hemophilia A who received general anesthesia for removal of foreign body from the nose. There was no excessive blood loss during surgery. Perioperatively, the patient received recombinant factor VIII coverage. Rest of the postoperative course was uneventful. Literature on the clinical management of patient with hemophilia A are reviewed and considerations for perioperative preparation and management of hemophilic patient are presented.
世界血友病联盟估计，全球有超过35万人患有某种形式的血友病。甲型血友病是一种出血性疾病，其表现范围从轻微创伤后持续出血到自发性出血。我们报告一例甲型血友病男性患者，因鼻腔异物取出接受全身麻醉。手术期间无过多失血。围手术期，患者接受了重组凝血因子VIII替代治疗。术后其余过程顺利。本文回顾了甲型血友病患者临床管理的相关文献，并提出了血友病患者围手术期准备和管理的注意事项。
