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人鱼序列征:一例病史

The sirenomelia sequence: a case history.

作者信息

Fadhlaoui Anis, Khrouf Mohamed, Gaigi Soumaya, Zhioua Fethi, Chaker Anis

机构信息

Department of Gynecology and Obstetrics, Aziza Othmana Hospital, Place du Gouvernement, La Kasba, Tunis, Tunisia.

出版信息

Clin Med Insights Case Rep. 2010;3:41-9. doi: 10.4137/ccrep.s5347. Epub 2010 Aug 13.

DOI:10.4137/ccrep.s5347
PMID:21769253
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3046016/
Abstract

We report a case of sirenomelia sequence observed in an incident of preterm labor during the 29th gestational week. According to some authors, this syndrome should be classified separately from caudal regression syndrome and is likely to be the result of an abnormality taking place during the fourth gestational week, causing developmental abnormalities in the lower extremities, pelvis, genitalia, urinary tract and digestive organs. Despite recent progress in pathology, the etiopathogenesis of sirenomelia is still debated.

摘要

我们报告一例在孕29周早产事件中观察到的并腿畸形序列征病例。根据一些作者的观点,该综合征应与尾椎退化综合征分开分类,并且很可能是妊娠第四周发生的异常所致,导致下肢、骨盆、生殖器、泌尿系统和消化器官发育异常。尽管病理学方面最近有进展,但并腿畸形的病因发病机制仍存在争议。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab24/3046016/71d43456be85/ccrep-2010-041f5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab24/3046016/68b899286f12/ccrep-2010-041f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab24/3046016/7cf4eecc2e1e/ccrep-2010-041f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab24/3046016/125c8abb9af8/ccrep-2010-041f3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab24/3046016/eb9df3444479/ccrep-2010-041f4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab24/3046016/71d43456be85/ccrep-2010-041f5.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab24/3046016/68b899286f12/ccrep-2010-041f1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab24/3046016/7cf4eecc2e1e/ccrep-2010-041f2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab24/3046016/125c8abb9af8/ccrep-2010-041f3.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab24/3046016/eb9df3444479/ccrep-2010-041f4.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ab24/3046016/71d43456be85/ccrep-2010-041f5.jpg

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