Hsu W Y, Chen J Y, Chi C S, Wong T T
Department of Pediatrics, Chung Shan Medical and Dental College Hospital, Taichung, R.O.C.
Zhonghua Yi Xue Za Zhi (Taipei). 1990 Jul;46(1):61-4.
A 12-year-old boy had a long history of headache since the age of 4 years. Numbness and weakness of the upper extremities and chest tightness, especially in the morning, were noted since 2 years ago. The headache became more severe and frequent and attacked even in sleep since one year ago. Arnold-Chiari type 1 malformation, cervical syringomyelia and mild hydrocephalus were demonstrated by MRI scan of the central nervous system. Headache and other symptoms disappeared immediately after surgical intervention. The formation of syringomyelia may be multifactorial, but Arnold-Chiari type 1 malformation and uneventful birth history play an important role in the underlying cause of this case. We presented this youngest case who had Arnold-Chiari type 1 malformation and onset of headache from the age of 4 years, discussed the pathogenesis of syringomyelia and reviewed the literature.
一名12岁男孩自4岁起就有长期头痛史。自2年前开始出现上肢麻木、无力以及胸闷，尤其是在早晨。自1年前起，头痛变得更加严重且频繁，甚至在睡眠中也会发作。中枢神经系统的MRI扫描显示为1型阿诺德-基亚里畸形、颈段脊髓空洞症和轻度脑积水。手术干预后，头痛和其他症状立即消失。脊髓空洞症的形成可能是多因素的，但1型阿诺德-基亚里畸形和顺产史在该病例的潜在病因中起重要作用。我们报告了这例最年轻的1型阿诺德-基亚里畸形且4岁起就出现头痛的病例，讨论了脊髓空洞症的发病机制并回顾了相关文献。
