Department of Maxillofacial and Plastic Surgery, Children Hospital Armand-Trousseau, Medical School Pierre and Marie-Curie, University Paris 6, Paris Cedex 12, France.
Int J Oral Maxillofac Surg. 2012 Feb;41(2):261-4. doi: 10.1016/j.ijom.2011.03.019. Epub 2011 Jul 28.
Chondrolipoma is a rare condition; especially in the oral cavity. The authors described a giant chondrolipoma of the tongue, associated with mandibular and lower lip overgrowth, in a 14-year-old boy. After tumour excision, histopathological examination showed mature cartilage within lobules of mature adipocytes. This is the first case of giant chondrolipoma associated with facial overgrowth. The aetiology and the association with a localized Proteus syndrome are discussed.
软骨脂肪瘤是一种罕见的疾病;特别是在口腔内。作者描述了一例 14 岁男孩舌部巨大软骨脂肪瘤,伴有下颌骨和下唇过度生长。肿瘤切除后,组织病理学检查显示成熟脂肪细胞小叶内有成熟软骨。这是首例与面部过度生长相关的巨大软骨脂肪瘤病例。讨论了其病因和与局部 Proteus 综合征的关系。